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KMID : 1103720230840030757
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Journal of the Korean Society of Radiology
2023 Volume.84 No. 3 p.757 ~ p.762
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Erdheim?Chester Disease Involving the Biliary System and Mimicking Immunoglobulin G4-Related Disease: A Case Report
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Hong Hyuk-Gi
Chung Yong-Eun
Rha Sun-Young
Hong Peng
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Abstract
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First described in 1930 as a lipoid granulomatosis, Erdheim-Chester disease (ECD) is a rare histiocytosis encompassing a group of disorders caused by overproduction of histiocytes, a subtype of white blood cells. This disease most commonly involves the bones and can affect organs in the abdomen; however, biliary involvement is rarely reported. We report a case of ECD with biliary involvement, which rendered it difficult to radiologically distinguish ECD from immunoglobulin G4-related disease.
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KEYWORD
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Erdheim-Chester Disease, Histiocytes, Immunoglobulin G4-Related Disease
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